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The retina lies in the back of the eye and is a multi-layered tissue
which detects visual images and transmits them to the brain. Retinitis
pigmentosa (RP) refers to a group of related diseases which tend
to run in families and cause slow but progressive loss of vision.
In retinitis pigmentosa, there is gradual destruction of some of
the nervous sensors in the retina.
The first symptoms usually occur in youth or young adulthood, although
it may be first seen at any age. Retinitis pigmentosa causes night
blindness and loss of side vision. In normal persons, the visual
system adjusts to darkness after a short period of time. People
with night blindness adjust to darkness very slowly, or not at all.
Due to the loss of side vision (peripheral vision) in patients with
retinitis pigmentosa, mobility becomes more difficult.
Most forms of retinitis pigmentosa are inherited. Different patterns
of heredity are associated with different degrees of progression.
An attempt to know more about how severely the disease has affected
other family members may help predict how a specific person might
ultimately be afflicted, though variability exists within each family.
Such knowledge is also helpful in making decisions about such things
as marriage, family and occupation.
In general, there is no specific treatment. Recent research suggests
that some patients may benefit from certain kinds of vitamin therapy.
But these studies are not conclusive. Much research is directed
toward solving this problem. Periodic examinations by an eye doctor
are advised.
It is important to keep in mind that patients with retinitis pigmentosa
may develop other treatable disease, such as glaucoman or cataracts.
Low vision aids may be prescribed. In some cases, retinitis pigmentosa
may be associated with other disease processes which might need
evaluation by other medical specialists.
Despite visual impairment, the many rehabilitative services that
are available today allow patients with retinitis pigmentosa to
live meaningful and rewarding lives.
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